Fulminant hemophagocytic lymphohistiocytosis secondary to a reactivated EBV infection: A case report

نویسندگان

  • Pantelis Antonodimitrakis
  • Cecilia Wassberg
  • Spyridon Gerovasileiou
  • Johan Back
  • Roger Hällgren
  • Björn Olsen
چکیده

Hemophagocytic lymphohistiocytosis (HLH) is an aggressive inflammatory syndrome that results from inappropriate activation of the immune system. HLH has a high mortality if not treated. We describe a case of a fulminant HLH, associated with a reactivation of an EBV infection. The patient responded well to steroid treatment.

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عنوان ژورنال:

دوره 118  شماره 

صفحات  -

تاریخ انتشار 2013